The operation for this condition
is very complex and involves reconstruction of the doors of the
tricuspid valve to make it functional and prevent the leak.
Bundle of Kent
Ebstein Anomaly is associated with the presence of an electric
connection between the right atrium and right ventricle via a
bundle called Bundle on Kent. This makes the electric impulse
bypass its usual course. This predisposes the child to have a
condition called Wolf Parkinson White Syndrome (WPW) and Supraventricular
One very important condition
which is associated with Ebstein Anomaly is a heart arythmia
which is called Wolf-Parkinson-Wide Syndrome (WPW Syndrome) which
disposes the heart to beat irregularly very fast and produce
a condition called Supra Vetricular Tachycardia (SVT).
This arythmia may be very difficult
to control especially in this condition and can sometimes require
multiple, sometimes lots, of medications.