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What is Marfan Syndrome? | Abnormalities: Heart : Skeletal : Eye : Other
Causes | Risks | Management | Surgery

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Marfan Syndrome: Surgery

Indications for Surgery

  • Thoracic aorta dilated
    to 5-6 cm.
  • Severe aortic regurgitation

Indications for Surgery

  • Family history of aortic dissection
  • The need for other major surgery

Emergency Surgery Indicated

  • Proximal dissection (large dissection that begins near the heart)
  • Or the tear is very extensive and they continue to have pain even after the blood pressure has been brought down to a low level
  • Surgery would be considered if the tear in the descending aorta seems to stabilize, but then grows progressively
  • Organ ischemia (kidneys, bowel, and spinal cord) will also require urgent surgery.
  • Evidence of fluid in the pericardial sac around the heart with a dissection that comes back to the heart, which suggests that, the tear is going into the pericardial space.

Emergency Surgery Indicated

  • Evidence of marked enlargement of the dissected aorta (aneurysm formation).
  • Evidence of blood leakage into tissue by contrast CT scan or transesophogeal echocardiogram.
  • Evidence that blood flow to one or more vital organs is being compromised.
  • Evidence of an intramural hematoma, a localized collection of blood within the aortic wall that can accumulate before the dissection progresses along the length of the aorta. Intramural hematomas indicate an impending dissection, and should be treated in an identical manner.

How successful is aortic surgery?

The survival rate for elective surgery for ascending aortic aneurysms is greater than 95 percent.
   


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