The most important part of this condition is to watch the aortic root dilation. There are normal measurements for the aortic root at every age and size and the doctors will be monitoring how wide the root of the aortic is (how dialated it is) at almost every 6 months to one year they may want to do an ultrasound to determine the extent of that dialation.

Should the width reach a size above 5 centimeters (the normal size is 2.5 centimeters or 1 inch in an adult) the doctors may recommend replacing the root of the aorta.