• The Heart House
Home

Problems with the Doors

1. Tricuspid Valve

The Tricuspid Valve is located between the right atrium and right ventricle. If this door is not developed this condition is called Atresia (Tricuspid Valve Atresia). There is a 3-step procedure to fix this defect:

Stage 1: Shunt Operation

Stage 2: Glenn Operation

Stage 3: Fontan Operation

Since the door did not develop in the baby before birth there was no blood coming from the right atrium to the right ventricle so the right ventricle became underdeveloped (hypoplastic right ventricle).

If the tricuspid door is displaced downward from it's usual location, this will result in the right atrium becoming excessively large and the right ventricle small and underdeveloped. This condition is called Ebstein Anomaly.

2. Mitral Valve

The mitral valve is the door between the left atrium and the left ventricle. If the mitral valve does not develop during the very early gestation weeks, the blood in the left atrium will not flow to the left ventricle, and therefore the left ventricle will be small and underdeveloped (Hypoplastic Left Heart Syndrome). There is a 3-step procedure to fix this defect:

Stage 1: Norwood Operation

Stage 2: Glenn Operation

Stage 3: Fontan Operation

3. Pulmonic Valve

The pulmonic valve is the door located between the right ventricle and the main pulmonary artery. If this door is a little bit small (depending on how small it is) we call this condition stenosis (Pulmonic Valve Stenosis). If it does not develop at all we call this condition atresia (Pulmonic Valve Atresia).

4. Aortic Valve

The aortic valve is the door located between the left ventricle and the aorta. If the valve is small this condition is called stenosis (Aortic Valve Stenosis). If this valve does not develop at all this condition is called atresia (Aortic Valve Atresia).

Tricuspid Valve Atresia

top

Pulmonary Valve Stenosis

top

Aortic Valve Stenosis

top

Quick Links

Contact Us

Children's Heart Institute

P. O. Box 10066 McLean, VA 22102

Central Registration (patient appointments):

phone - 703-481-5801

Billing Inquiries:

phone - 571-612-2600 / fax - 571-266-4096